Management of mandibular infantile desmoid fibromatosis: A pediatric case report.

Journal: International journal of surgery case reports
Published Date:

Abstract

INTRODUCTION: Infantile desmoid fibromatosis (IDF) is a rare, benign soft tissue tumor, with locally infiltrative behavior. It presents two forms: solitary and disseminated. This condition can affect any location, although IDF of the mandibular is exceptionally rare. Its locally aggressive nature and proximity to critical anatomical structures present significant management challenges. Its management modalities are still controverted.

Authors

  • Rania Kharrat
    ENT department and research Laboratory LR23ES01, Habib Bourguiba University Hospital, University of Sfax, Sfax, Tunisia. Electronic address: kharratrania@yahoo.com.
  • Mohamed Amine Chaabouni
    ENT department and research Laboratory LR23ES01, Habib Bourguiba University Hospital, University of Sfax, Sfax, Tunisia. Electronic address: chaabouni_moh_amin@medecinesfax.org.
  • Yasmine Sghaier
    ENT department and research Laboratory LR23ES01, Habib Bourguiba University Hospital, University of Sfax, Sfax, Tunisia. Electronic address: Yasminesghaier18@gmail.com.
  • Ines Akrout
    ENT department and research Laboratory LR23ES01, Habib Bourguiba University Hospital, University of Sfax, Sfax, Tunisia. Electronic address: akrout2803@yahoo.com.
  • Bouthaina Hammami
    ENT department and research Laboratory LR23ES01, Habib Bourguiba University Hospital, University of Sfax, Sfax, Tunisia. Electronic address: bouthainahk@gmail.com.
  • Ilhem Charfeddine
    ENT department and research Laboratory LR23ES01, Habib Bourguiba University Hospital, University of Sfax, Sfax, Tunisia. Electronic address: Charfeddine_ilhem@medecinesfax.org.

Keywords

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