Incessant Pericarditis With Recurrent Cardiac Tamponade as the Manifestation of Autoimmune Polyglandular Syndrome Type II.

Journal: JACC. Case reports
Published Date:

Abstract

A 23-year-old man was admitted for acute pericarditis that evolved to cardiac tamponade and shock with need of emergent pericardiocentesis and inotropic support. Corticosteroid therapy was successful, but despite a gradual tapering, the patient relapsed. Incidentally, the patient developed hyperkalemia with hyponatremia. Subsequent hormonal measurements confirmed autoimmune polyglandular syndrome type-2. ().

Authors

  • Ana V Marinho
    Cardiology Unit, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal.
  • Rui Baptista
    Cardiology Unit, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal.
  • Luís Cardoso
    Endocrinology Department, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal.
  • Patrícia M Alves
    Cardiology Unit, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal.
  • Sílvia Monteiro
    Cardiology Unit, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal.
  • Francisco Gonçalves
    Cardiology Unit, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal.
  • Lino Gonçalves
    Cardiology Unit, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal.

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