NOVEL MUTATIONS IN AN INFANT WITH MICROCEPHALIC PRIMORDIAL DWARFISM, DILATED CARDIOMYOPATHY, SUBCLINICAL HYPOTHYROIDISM, AND EARLY DEATH: EXPANDING THE PHENOTYPE OF MUTATIONS.

Journal: AACE clinical case reports
Published Date:

Abstract

OBJECTIVE: Microcephalic primordial dwarfism (MPD) is a group of clinically and genetically heterogeneous disorders which result in severe prenatal and postnatal growth failure. X-ray repair cross-complementing protein 4 () is a causative gene for an autosomal recessive form of MPD. The objective of this report is to describe novel mutations in a female infant with MPD, dilated cardiomyopathy, and subclinical hypothyroidism.

Authors

  • Meghan E Fredette
  • Kristin C Lombardi
  • Angela L Duker
  • Catherine O Buck
  • Chanika Phornphutkul
  • Michael B Bober
  • Jose Bernardo Quintos

Keywords

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