Robotic and clinical evaluation of upper limb motor performance in patients with Friedreich's Ataxia: an observational study.

Journal: Journal of neuroengineering and rehabilitation
Published Date:

Abstract

BACKGROUND: Friedreich's ataxia (FRDA) is the most common hereditary autosomal recessive form of ataxia. In this disease there is early manifestation of gait ataxia, and dysmetria of the arms and legs which causes impairment in daily activities that require fine manual dexterity. To date there is no cure for this disease. Some novel therapeutic approaches are ongoing in different steps of clinical trial. Development of sensitive outcome measures is crucial to prove therapeutic effectiveness. The aim of the study was to assess the reliability and sensitivity of quantitative and objective assessment of upper limb performance computed by means of the robotic device and to evaluate the correlation with clinical and functional markers of the disease severity.

Authors

  • Marco Germanotta
    Don Carlo Gnocchi Onlus Foundation, Piazzale Morandi 6, 20121, Milan, Italy. mgermanotta@dongnocchi.it.
  • Gessica Vasco
    Movement Analysis and Robotics Laboratory (MARLab), Neurorehabilitation Units, IRCCS Bambino Gesù Children's Hospital, Via Torre di Palidoro, 00050, Passoscuro (Fiumicino), Rome, Italy. gessica.vasco@opbg.net.
  • Maurizio Petrarca
    Movement Analysis and Robotics Laboratory (MARLab), Neurorehabilitation Units, IRCCS Bambino Gesù Children's Hospital, Via Torre di Palidoro, 00050, Passoscuro (Fiumicino), Rome, Italy. maurizio.petrarca@opbg.net.
  • Stefano Rossi
  • Sacha Carniel
    Movement Analysis and Robotics Laboratory (MARLab), Neurorehabilitation Units, IRCCS Bambino Gesù Children's Hospital, Via Torre di Palidoro, 00050, Passoscuro (Fiumicino), Rome, Italy. sacha26304@yahoo.it.
  • Enrico Bertini
    Unit of Neuromuscular and Neurodegenerative Disorders, Laboratory of Molecular Medicine, IRCCS Bambino Gesù Children's Hospital, Piazza S. Onofrio 4, 00165, Rome, Italy. enricosilvio.bertini@opbg.net.
  • Paolo Cappa
  • Enrico Castelli